PINX1

PIN2 (TERF1) interacting telomerase inhibitor 1

Summary

Enables telomerase RNA binding activity and telomerase inhibitor activity. Involved in several processes, including negative regulation of macromolecule metabolic process; positive regulation of protein localization to nucleolus; and protein localization to organelle. Acts upstream of or within telomere maintenance via telomerase. Located in several cellular components, including chromosomal region; nuclear lumen; and spindle. Implicated in hepatocellular carcinoma. [provided by Alliance of Genome Resources, Apr 2025]

Known Variants59 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14514787688:10,622,925T/Cuncertain significance
rs2020727778:10,622,935C/Guncertain significance
rs7619908488:10,622,987T/Guncertain significance
rs7731377408:10,623,008C/Guncertain significance
rs5635132698:10,623,031G/Tuncertain significance
rs13967182938:10,623,042C/Tuncertain significance
rs3688439058:10,623,050G/Auncertain significance
rs5425060778:10,623,083G/Alikely benign
rs18010097028:10,623,129C/Guncertain significance
rs14107224408:10,623,131G/Auncertain significance
rs3772608668:10,623,134G/Auncertain significance
rs2022026908:10,623,135C/Tuncertain significance
rs5304427358:10,623,136G/Tlikely benign
rs11865612688:10,623,165C/Auncertain significance
rs1127213048:10,623,168C/Tlikely benign
rs18010129608:10,623,187C/Guncertain significance
rs15631973198:10,623,188T/Cuncertain significance
rs7777342308:10,623,191G/Alikely benign
rs7718449338:10,623,193G/Cuncertain significance
rs7737168028:10,623,210G/Tuncertain significance
rs171523228:10,623,214G/Cbenign
rs12973667238:10,623,230T/Auncertain significance
rs7521107098:10,623,299G/Cuncertain significance
rs2003918968:10,623,309C/Auncertain significance
rs3769550608:10,623,335G/Auncertain significance
rs7540267598:10,623,381T/Cuncertain significance
rs5649066178:10,623,483G/T
rs112500728:10,632,121C/Tdownstream gene variant
rs112500738:10,632,236G/A
rs285649798:10,633,960C/T
rs78141428:10,637,552G/Aupstream gene variant
rs132722968:10,639,942T/C
rs18210028:10,640,065C/A
rs100957378:10,641,152G/Aregulatory region variant
rs119986068:10,663,120C/G
rs787713338:10,663,160C/G
rs28982458:10,666,174G/Aintron variant
rs66015308:10,671,272G/Aregulatory region variant
rs346531708:10,676,542G/A
rs7545374808:10,677,705C/Guncertain significance
rs17978245818:10,677,711T/Cuncertain significance
rs3737877988:10,677,722T/Cuncertain significance
rs78407858:10,683,127C/G
rs25359956638:10,683,667G/Auncertain significance
rs9387172648:10,683,745T/Cuncertain significance
rs3759165958:10,683,748G/Auncertain significance
rs117767678:10,683,929G/A
rs69915268:10,689,050T/Cintron variant
rs13122919338:10,689,177G/Auncertain significance
rs2017848038:10,689,208C/Tuncertain significance
rs3733313838:10,690,409T/Cuncertain significance
rs3777154998:10,690,422C/Tuncertain significance
rs5557505448:10,690,433T/Auncertain significance
rs7564457218:10,690,447T/Auncertain significance
rs12423419598:10,690,472C/Tuncertain significance
rs7600823228:10,692,178T/Cuncertain significance
rs48405198:10,693,113T/A
rs350919298:10,693,492T/A
rs767857578:10,693,690A/Gupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.