SHARPIN

SHANK associated RH domain interactor

Summary

Enables polyubiquitin modification-dependent protein binding activity. Involved in defense response to bacterium; protein linear polyubiquitination; and regulation of signal transduction. Located in cytosol. Part of LUBAC complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants41 total

rsidPosition (GRCh37)AllelesClassClinVar
rs3680011648:145,153,848G/Cuncertain significance
rs1125522788:145,153,851C/Tlikely benign
rs9259282468:145,153,884C/Tuncertain significance
rs7528874358:145,153,989G/Auncertain significance
rs2003440628:145,154,070C/Tuncertain significance
rs7515543698:145,154,086G/Cuncertain significance
rs5625332428:145,154,186C/Auncertain significance
rs346747528:145,154,222G/Abenign
rs10440926038:145,154,260C/Tuncertain significance
rs773598628:145,154,282G/Amissense variant
rs2007774358:145,154,296C/Tuncertain significance
rs13574318658:145,154,438C/Tuncertain significance
rs3693351558:145,154,447T/Cuncertain significance
rs7617383338:145,154,488G/Alikely benign
rs18362480068:145,154,622G/Auncertain significance
rs25373365178:145,154,627C/Guncertain significance
rs3754422638:145,154,658C/Tuncertain significance
rs25373367488:145,154,688G/Cuncertain significance
rs2007022538:145,154,697C/Guncertain significance
rs3680296458:145,154,715C/Tuncertain significance
rs7679437958:145,154,723C/Tlikely benign
rs3717566778:145,154,724G/Auncertain significance
rs1999321768:145,154,823C/Abenign
rs12184300638:145,154,836C/Guncertain significance
rs10242479668:145,154,857C/Guncertain significance
rs25373372098:145,154,865G/Auncertain significance
rs2016229768:145,154,925C/Tuncertain significance
rs7755483238:145,154,927G/Auncertain significance
rs2012942908:145,154,967T/Cuncertain significance
rs125507298:145,155,408C/G
rs3737350128:145,157,977C/Auncertain significance
rs8965115128:145,158,040C/Guncertain significance
rs7732254478:145,158,053G/Auncertain significance
rs125491498:145,158,446C/Tbenign
rs12311679038:145,158,473C/Guncertain significance
rs111362548:145,158,503G/Tbenign
rs2009728568:145,158,514G/Clikely benign
rs9965821448:145,158,563C/Guncertain significance
rs341730628:145,158,607G/Abenign
rs9481424948:145,158,635C/Tuncertain significance
rs111362568:145,160,646T/Cbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.