TGM2

transglutaminase 2

Summary

Transglutaminases are enzymes that catalyze the crosslinking of proteins by epsilon-gamma glutamyl lysine isopeptide bonds. While the primary structure of transglutaminases is not conserved, they all have the same amino acid sequence at their active sites and their activity is calcium-dependent. The protein encoded by this gene acts as a monomer, is induced by retinoic acid, and appears to be involved in apoptosis. Finally, the encoded protein is the autoantigen implicated in celiac disease. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]

Known Variants75 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14450103820:36,758,627G/Alikely benign
rs15018661320:36,758,680C/Tuncertain significance
rs37045325020:36,758,717C/Tlikely benign
rs119587064620:36,758,758C/Tuncertain significance
rs222947220:36,758,762G/Abenign
rs120439562120:36,758,766T/Cuncertain significance
rs92423448520:36,758,770G/Auncertain significance
rs37717005120:36,759,502C/Guncertain significance
rs14358099720:36,759,503C/Tbenign
rs251558471520:36,759,531C/Guncertain significance
rs74714434020:36,759,612T/Auncertain significance
rs15071284420:36,760,743C/Tuncertain significance
rs251558723720:36,760,752A/Guncertain significance
rs37080394620:36,760,786C/Tuncertain significance
rs14948097920:36,760,809G/Auncertain significance
rs19983245220:36,760,882T/Cuncertain significance
rs222947320:36,760,894C/Abenign
rs14017190220:36,766,591G/Alikely benign
rs92613293620:36,766,613C/Tuncertain significance
rs75639662520:36,766,632C/Tuncertain significance
rs75780933420:36,766,643G/Tuncertain significance
rs74902277420:36,766,783G/Tlikely benign
rs53528047920:36,767,854G/Alikely benign
rs4562163420:36,767,908G/Tbenign
rs75994175620:36,767,955C/Tuncertain significance
rs222947020:36,767,986C/Tbenign
rs251559988120:36,768,003T/Cuncertain significance
rs77613203020:36,768,021T/Guncertain significance
rs7861999120:36,768,026C/Tbenign
rs77287422520:36,768,052C/Tlikely benign
rs119634966820:36,769,744G/Alikely benign
rs20136957320:36,769,748C/Tlikely benign
rs75524887720:36,770,476C/Tuncertain significance
rs222947120:36,770,483G/Abenign
rs20206750420:36,770,519C/Tbenign
rs14298762720:36,770,546A/Glikely benign
rs75793803920:36,770,553G/Auncertain significance
rs14020373320:36,770,573G/Alikely benign
rs4544220220:36,775,132G/Abenign
rs75170875720:36,775,166C/Tuncertain significance
rs77821191820:36,775,176C/Tuncertain significance
rs36998885920:36,775,234G/Alikely benign
rs54963136020:36,775,243G/Abenign
rs78069782220:36,775,259C/Tuncertain significance
rs4546169120:36,776,393G/Cbenign
rs76858357020:36,776,418C/Tuncertain significance
rs77002992120:36,776,423G/Alikely benign
rs76463045320:36,779,426C/Tuncertain significance
rs20044606020:36,779,458C/Tbenign
rs602352620:36,783,582T/G
rs19065861320:36,784,246C/Tlikely benign
rs75899603820:36,784,311C/Tuncertain significance
rs76400829120:36,784,335C/Auncertain significance
rs14613736520:36,784,354C/Tlikely benign
rs15090928920:36,784,379C/Tlikely benign
rs54032002120:36,784,380G/Auncertain significance
rs13939506620:36,784,408C/Tuncertain significance
rs75525605920:36,784,410G/Auncertain significance
rs4127472020:36,784,455C/Tbenign
rs37651050020:36,784,456G/Auncertain significance
rs14447678820:36,784,469G/Abenign
rs481152820:36,787,429G/Aregulatory region variant
rs20159751120:36,789,869C/Tuncertain significance
rs75586529520:36,789,870G/Auncertain significance
rs133374841420:36,789,872C/Tuncertain significance
rs75363095520:36,789,912G/Tlikely benign
rs14471576520:36,789,928C/Tbenign
rs76200683820:36,789,929C/Tuncertain significance
rs20020676420:36,789,939C/Tuncertain significance
rs95095512220:36,789,947T/Cuncertain significance
rs75829843720:36,789,956C/Tuncertain significance
rs14285166620:36,790,128G/Aintron variant
rs727078520:36,791,619G/Tintron variant
rs207638020:36,793,529G/T
rs18945509220:36,793,740A/Cregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.