TMEM163

transmembrane protein 163

Summary

Predicted to enable zinc ion binding activity. Involved in myelination and zinc export across plasma membrane. Predicted to be located in early endosome membrane. Predicted to be active in plasma membrane and synaptic vesicle membrane. Implicated in hypomyelinating leukodystrophy 25. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants36 total

rsidPosition (GRCh37)AllelesClassClinVar
rs13640598302:135,214,321A/Guncertain significance
rs11999225362:135,214,322C/Tuncertain significance
rs7566537552:135,214,327G/Auncertain significance
rs101796862:135,214,570C/Tdownstream gene variant
rs24683923812:135,215,618A/Tuncertain significance
rs16864414002:135,215,628G/Cuncertain significance
rs7651960212:135,215,660T/Cuncertain significance
rs1458093132:135,215,721C/Tuncertain significance
rs2017688332:135,223,739C/Tuncertain significance
rs7678491592:135,260,549C/Tuncertain significance
rs24684509472:135,260,564A/Cuncertain significance
rs561314902:135,263,081G/Aintron variant
rs4874042:135,300,861A/T
rs1480402532:135,308,153T/Cuncertain significance
rs24685088482:135,308,162T/Cpathogenic
rs24685088502:135,308,165A/Tuncertain significance
rs24685088862:135,308,187G/Apathogenic
rs8423492:135,342,452G/Tintron variant
rs8423572:135,345,059G/Aintron variant
rs18186132:135,356,285G/A
rs1873819782:135,377,597C/Gintron variant
rs177896332:135,386,474A/Cintron variant
rs67397062:135,407,409A/Cintron variant
rs621713672:135,408,637G/A
rs75607382:135,419,163A/Gintron variant
rs9984512:135,429,288G/Aregulatory region variant
rs49541622:135,438,789G/Aintron variant
rs24673256712:135,470,865A/Gpathogenic
rs7531631322:135,476,315A/Cuncertain significance
rs13367360912:135,476,348C/Tuncertain significance
rs16850971402:135,476,353C/Guncertain significance
rs12910250652:135,476,366T/Auncertain significance
rs9466265602:135,476,396C/Tuncertain significance
rs12529033872:135,476,406C/Guncertain significance
rs10565881592:135,476,420G/Auncertain significance
rs8879195852:135,476,466C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.