ACSL5

acyl-CoA synthetase long chain family member 5

Summary

The protein encoded by this gene is an isozyme of the long-chain fatty-acid-coenzyme A ligase family. Although differing in substrate specificity, subcellular localization, and tissue distribution, all isozymes of this family convert free long-chain fatty acids into fatty acyl-CoA esters, and thereby play a key role in lipid biosynthesis and fatty acid degradation. This isozyme is highly expressed in uterus and spleen, and in trace amounts in normal brain, but has markedly increased levels in malignant gliomas. This gene functions in mediating fatty acid-induced glioma cell growth. Three transcript variants encoding two different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]

Known Variants47 total

rsidPosition (GRCh37)AllelesClassClinVar
rs241962110:114,135,013C/Tregulatory region variant
rs76108087010:114,136,075C/Tlikely benign
rs249315371410:114,136,077C/Guncertain significance
rs75441283410:114,136,103C/Auncertain significance
rs136375116710:114,136,127G/Cuncertain significance
rs20059952810:114,136,132C/Tlikely benign
rs7967162310:114,141,103G/Aintron variant
rs76203067110:114,154,742C/Tuncertain significance
rs7947434210:114,154,823C/Abenign
rs132902041510:114,154,837A/Guncertain significance
rs1119594510:114,155,586C/G
rs74673188510:114,158,705G/Cuncertain significance
rs6187235510:114,160,713G/Cintron variant
rs1222108510:114,163,320A/Gdownstream gene variant
rs53145595110:114,164,298C/Auncertain significance
rs74536868710:114,164,499T/Guncertain significance
rs241962610:114,167,216G/Adownstream gene variant
rs20134732010:114,168,170C/Tbenign
rs14001139210:114,168,208C/Tuncertain significance
rs126105713810:114,168,213T/Auncertain significance
rs75457049510:114,168,253A/Cuncertain significance
rs373694710:114,169,190C/Acoding sequence variant
rs20024788710:114,169,273G/Auncertain significance
rs184412947510:114,169,283T/Cuncertain significance
rs75123017710:114,169,355T/Auncertain significance
rs37524229510:114,169,440T/Alikely benign
rs77070450610:114,170,350C/Guncertain significance
rs138230361310:114,171,673C/Tuncertain significance
rs156474021710:114,171,678C/Guncertain significance
rs1119595210:114,173,554G/T
rs450192310:114,174,431A/Cintron variant
rs1181226110:114,176,693G/Abenign
rs14818071910:114,176,715G/Auncertain significance
rs249327639110:114,177,620G/Tuncertain significance
rs37240369510:114,177,631A/Tuncertain significance
rs133610063610:114,181,394C/Apathogenic
rs76424552810:114,181,417A/Guncertain significance
rs249328892610:114,181,741A/Guncertain significance
rs128187187010:114,181,768A/Guncertain significance
rs1225491510:114,181,773A/Gbenign
rs249331134210:114,185,115T/Cuncertain significance
rs14423626210:114,185,175T/Cuncertain significance
rs75207261210:114,185,231A/Cuncertain significance
rs11140186010:114,185,237C/Tuncertain significance
rs184470711410:114,186,062C/Tuncertain significance
rs78177805710:114,186,092C/Tuncertain significance
rs148535295110:114,187,036A/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.