BCAM

basal cell adhesion molecule (Lutheran blood group)

Summary

This gene encodes Lutheran blood group glycoprotein, a member of the immunoglobulin superfamily and a receptor for the extracellular matrix protein, laminin. The protein contains five extracellular immunoglobulin domains, a single transmembrane domain, and a short C-terminal cytoplasmic tail. This protein may play a role in epithelial cell cancer and in vaso-occlusion of red blood cells in sickle cell disease. Polymorphisms in this gene define some of the antigens in the Lutheran system and also the Auberger system. Inactivating variants of this gene result in the recessive Lutheran null phenotype, Lu(a-b-), of the Lutheran blood group. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, May 2012]

Known Variants75 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7304825819:45,311,144C/Aregulatory region variant
rs56089865619:45,311,310T/G
rs171571801119:45,312,430C/Guncertain significance
rs18512296619:45,313,452C/Tregulatory region variant
rs13928902419:45,314,491C/Guncertain significance
rs14105361919:45,314,515C/Tlikely benign
rs2839965319:45,315,445G/Amissense variantbenign
rs77057036819:45,315,502G/Auncertain significance
rs75474389119:45,315,540C/Tuncertain significance
rs12191813319:45,315,576C/Tstop gainedpathogenic
rs20223329919:45,315,585G/Auncertain significance
rs75336363219:45,315,641C/Tlikely benign
rs77846531019:45,315,642G/Auncertain significance
rs20039871319:45,315,656T/Alikely benign
rs54662899919:45,315,740C/Tuncertain significance
rs52807079119:45,316,221A/G
rs37201993319:45,316,423C/A
rs196845262019:45,316,559A/Guncertain significance
rs2839965619:45,316,704T/Alikely benign
rs75044859919:45,316,712C/Guncertain significance
rs156857200319:45,316,715A/Guncertain significance
rs77589225619:45,316,759C/Glikely benign
rs12191813219:45,316,784C/Tstop gainedpathogenic
rs20012414319:45,316,785G/Cuncertain significance
rs381014119:45,316,804C/Tsynonymous variantbenign
rs381014019:45,316,807C/Tbenign
rs13927521219:45,316,825C/Gbenign
rs93740361219:45,316,827A/Tuncertain significance
rs14410505919:45,316,845T/Auncertain significance
rs75759947419:45,316,857C/Tuncertain significance
rs13961035119:45,317,448C/Tmissense variant
rs74837736719:45,317,453C/Tuncertain significance
rs996760119:45,317,469G/Abenign
rs20079494919:45,317,852G/Abenign
rs19023200119:45,317,894G/Auncertain significance
rs36865652919:45,317,925G/Auncertain significance
rs18201956119:45,317,934G/Auncertain significance
rs37549821719:45,317,935C/Tlikely benign
rs37120603219:45,317,969G/Auncertain significance
rs77790511819:45,318,009G/Alikely benign
rs18088745319:45,318,495A/Gintron variant
rs18885545519:45,321,790C/Guncertain significance
rs14197886819:45,321,822A/Tuncertain significance
rs2839962619:45,321,841G/Abenign
rs13830258719:45,321,856G/Auncertain significance
rs77422511019:45,322,016G/Auncertain significance
rs2839962919:45,322,030G/Tbenign
rs14403400419:45,322,059A/Guncertain significance
rs14867443519:45,322,070G/Alikely benign
rs76006267819:45,322,083C/Tuncertain significance
rs56026605219:45,322,113C/Auncertain significance
rs2839963019:45,322,327A/Clikely benign
rs196854267419:45,322,361G/Auncertain significance
rs2839963119:45,322,377C/Guncertain significance
rs37046872619:45,322,385C/Tuncertain significance
rs55773419619:45,322,405G/Auncertain significance
rs75990203719:45,322,434C/Auncertain significance
rs57790382419:45,322,442G/Auncertain significance
rs251368799019:45,322,675A/Cuncertain significance
rs113506219:45,322,744A/Gmissense variantbenign
rs14188662919:45,322,746C/Tlikely benign
rs15022092619:45,322,840G/Abenign
rs14741475519:45,322,910G/Auncertain significance
rs13974619219:45,322,913G/Auncertain significance
rs37295531219:45,322,931G/Alikely benign
rs76116532219:45,322,959G/Alikely benign
rs14209240519:45,323,344A/Gintron variant
rs20080165819:45,323,958C/Tlikely benign
rs19985407219:45,323,964C/Tlikely benign
rs77649423119:45,324,005C/Tuncertain significance
rs55419228719:45,324,008G/Auncertain significance
rs57410251919:45,324,017G/Auncertain significance
rs13984544719:45,324,071G/Alikely benign
rs20104933019:45,324,164G/Alikely benign
rs2839966519:45,324,897C/Tdownstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.