ERAP1

endoplasmic reticulum aminopeptidase 1

Summary

The protein encoded by this gene is an aminopeptidase involved in trimming HLA class I-binding precursors so that they can be presented on MHC class I molecules. The encoded protein acts as a monomer or as a heterodimer with ERAP2. This protein may also be involved in blood pressure regulation by inactivation of angiotensin II. Three transcript variants encoding two different isoforms have been found for this gene.[provided by RefSeq, Oct 2010]

Known Variants142 total

rsidPosition (GRCh37)AllelesClassClinVar
rs3990055:96,111,240T/A
rs131605625:96,111,371G/Adownstream gene variant
rs174813345:96,111,779A/Gbenign
rs1128552555:96,111,805G/Tbenign
rs105152485:96,112,005C/Tbenign
rs10654075:96,112,083T/Gbenign
rs15815184215:96,112,127C/Tlikely benign
rs1463334965:96,112,139G/Abenign
rs1395767685:96,112,182A/Glikely benign
rs5549337865:96,112,237A/Guncertain significance
rs7714089215:96,112,249C/Tuncertain significance
rs2003713295:96,112,264G/Alikely benign
rs562138135:96,112,284A/Tbenign
rs563251095:96,112,295C/Tbenign
rs270385:96,112,954A/Gdownstream gene variant
rs1494815:96,114,346A/T
rs13429469395:96,116,128T/Guncertain significance
rs3713939835:96,116,138G/Alikely benign
rs12144724155:96,116,157A/Cuncertain significance
rs1408653045:96,116,799G/Tlikely benign
rs174818565:96,116,808G/Abenign
rs800887865:96,116,854G/Abenign
rs7745538735:96,116,879C/Guncertain significance
rs270425:96,116,940A/Gbenign
rs270435:96,117,300G/Abenign
rs2017847105:96,117,388C/Tbenign
rs7667105385:96,117,414A/Glikely benign
rs1429852245:96,117,477A/Gbenign
rs9937034595:96,117,482T/Cuncertain significance
rs13345715805:96,117,491G/Auncertain significance
rs17752095815:96,117,512T/Cuncertain significance
rs1511034355:96,117,548C/Tuncertain significance
rs1464232385:96,118,811G/Abenign
rs25334052075:96,118,831C/Tuncertain significance
rs270445:96,118,852G/Cmissense variantbenign
rs174820785:96,118,866C/Tmissense variantbenign
rs7688423455:96,118,885C/Tuncertain significance
rs2008143575:96,119,579A/Tdownstream gene variant
rs1874474955:96,119,619G/Alikely benign
rs7612470445:96,119,716A/Tuncertain significance
rs1472527605:96,119,782A/Guncertain significance
rs398415:96,120,170G/C
rs4698765:96,121,406A/Gintron variantbenign
rs1113633475:96,121,496C/Tbenign
rs765980895:96,121,497G/Abenign
rs4697835:96,121,524C/Tbenign
rs2018562605:96,121,583C/Aconflicting classifications of pathogenicity
rs1493748915:96,121,596C/Auncertain significance
rs13949219075:96,121,605C/Alikely benign
rs1147033125:96,121,672A/Cbenign
rs11883435985:96,121,679G/Clikely benign
rs4697585:96,121,715C/Tbenign
rs9098160835:96,122,197C/Tuncertain significance
rs100508605:96,122,210C/Tmissense variantbenign
rs25334600785:96,122,219T/Cuncertain significance
rs11794166085:96,122,242T/Cuncertain significance
rs303795:96,122,260T/Gbenign
rs303805:96,122,281A/Cbenign
rs1686745:96,123,125T/Cdownstream gene variant
rs4677355:96,123,160T/Cdownstream gene variant
rs2464545:96,123,264C/Adownstream gene variant
rs617346135:96,124,247C/Tlikely benign
rs14290515725:96,124,277G/Cuncertain significance
rs22780175:96,124,296C/Gbenign
rs301875:96,124,330T/Cmissense variantbenign
rs786496525:96,124,373T/Clikely benign
rs301865:96,124,447G/Cbenign
rs265105:96,125,910C/Tbenign
rs5433635505:96,126,001A/Tuncertain significance
rs1447373045:96,126,041C/Tuncertain significance
rs14717445355:96,126,054C/Guncertain significance
rs277105:96,126,197A/Gbenign
rs275295:96,126,308A/Gsynonymous variantbenign
rs1843209645:96,126,328T/Cuncertain significance
rs25335195075:96,126,337T/Cuncertain significance
rs12292609145:96,127,788C/Auncertain significance
rs1463861795:96,127,799T/Cuncertain significance
rs32138095:96,127,833A/Gbenign
rs3766962685:96,127,865C/Tuncertain significance
rs1454584135:96,127,866G/Abenign
rs1816689025:96,127,868C/Tlikely benign
rs14171470885:96,127,874A/Guncertain significance
rs276405:96,127,905T/Cbenign
rs25335501065:96,129,129T/Cuncertain significance
rs274345:96,129,512A/Gsynonymous variantbenign
rs22879875:96,129,535T/Cmissense variantbenign
rs278955:96,129,543T/Cbenign
rs5566234435:96,129,625T/Clikely benign
rs5748108395:96,129,631C/Tuncertain significance
rs4697355:96,130,014T/A
rs266185:96,130,836T/Cmissense variantbenign
rs7773678835:96,130,846G/Auncertain significance
rs5765548605:96,130,859C/Guncertain significance
rs264895:96,133,427C/Tintron variant
rs20136715:96,134,283T/A
rs275285:96,136,525T/Cbenign
rs25336425975:96,136,570G/Tuncertain significance
rs5771503525:96,136,623C/Tuncertain significance
rs1397820605:96,136,668G/Cuncertain significance
rs1424826785:96,136,677G/Cbenign

Showing 100 of 142 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.