MGAT5

alpha-1,6-mannosylglycoprotein 6-beta-N-acetylglucosaminyltransferase

Summary

The protein encoded by this gene belongs to the glycosyltransferase family. It catalyzes the addition of beta-1,6-N-acetylglucosamine to the alpha-linked mannose of biantennary N-linked oligosaccharides present on the newly synthesized glycoproteins. It is one of the most important enzymes involved in the regulation of the biosynthesis of glycoprotein oligosaccharides. Alterations of the oligosaccharides on cell surface glycoproteins cause significant changes in the adhesive or migratory behavior of a cell. Increase in the activity of this enzyme has been correlated with the progression of invasive malignancies. [provided by RefSeq, Oct 2011]

Known Variants38 total

rsidPosition (GRCh37)AllelesClassClinVar
rs22778822:134,883,353C/T
rs1510881392:134,893,133C/Tintron variant
rs12571692:134,963,862C/T
rs1847209772:134,971,747T/Cintron variant
rs1113959972:135,000,907C/Tintron variant
rs25937042:135,005,277G/A
rs13970591082:135,011,981C/Tuncertain significance
rs24685299412:135,012,068T/Cuncertain significance
rs1414037712:135,012,114G/Auncertain significance
rs24420462:135,014,078G/A
rs24603832:135,014,126T/Cintron variant
rs12572192:135,014,890A/T
rs12998876732:135,028,071C/Tuncertain significance
rs7581831702:135,028,076A/Guncertain significance
rs5342582152:135,028,082G/Auncertain significance
rs1460629312:135,040,366A/Cregulatory region variant
rs129894562:135,042,375T/Cintron variant
rs126131402:135,061,644T/Aintron variant
rs49539112:135,068,794T/C
rs5705617892:135,072,760G/A
rs1463962882:135,075,135C/Tuncertain significance
rs14391092:135,083,922A/Gintron variant
rs2001478032:135,095,833G/Auncertain significance
rs7584541352:135,095,839C/Tuncertain significance
rs3745077342:135,095,855T/Guncertain significance
rs7658134082:135,095,911C/Tuncertain significance
rs2012248262:135,095,912G/Auncertain significance
rs24674655512:135,095,933T/Cuncertain significance
rs1420272972:135,095,944A/Cuncertain significance
rs1395982732:135,099,203A/Cuncertain significance
rs24674963072:135,099,317G/Auncertain significance
rs2015468552:135,102,625G/Cuncertain significance
rs124676092:135,143,287C/Tintron variant
rs1395347212:135,160,648C/Tlikely benign
rs7629558922:135,180,394C/Tlikely benign
rs7518394992:135,206,374G/Cuncertain significance
rs349445082:135,207,964C/T3 prime UTR variant
rs5395882:135,212,329G/A

Gene information from NCBI Gene. Variant classifications from ClinVar.