SP140

SP140 nuclear body protein

Summary

This gene encodes a member of the SP100 family of proteins, which are share common domains including an N-terminal homogeneously staining region domain followed by a SP100/autoimmune regulator/NucP41/P75/deformed epidermal autoregulatory factor domain, a plant homeobox zinc finger, and a bromodomain. The encoded protein is interferon-inducible and is expressed at high levels in the nuclei of leukocytes. Variants of this gene have been associated with multiple sclerosis, Crohn's disease, and chronic lymphocytic leukemia. Alternative splicing results in multiple variants. [provided by RefSeq, Aug 2016]

Known Variants56 total

rsidPosition (GRCh37)AllelesClassClinVar
rs24702462172:231,090,587A/Tuncertain significance
rs67167532:231,097,129T/Cintron variant
rs1156181782:231,101,855T/Gbenign
rs7788482552:231,101,947G/Auncertain significance
rs3776275512:231,102,983T/Cuncertain significance
rs11797782312:231,103,014G/Tuncertain significance
rs14814177352:231,103,052T/Cuncertain significance
rs8896532812:231,106,136C/Tuncertain significance
rs1892969912:231,106,154G/Tuncertain significance
rs3736875172:231,106,181T/Auncertain significance
rs751777762:231,106,210T/Cbenign
rs102018722:231,106,724C/Tintron variant
rs9052235232:231,108,500T/Guncertain significance
rs5300693912:231,112,645G/Alikely benign
rs3693903602:231,112,681C/Guncertain significance
rs3712398982:231,113,616A/Glikely benign
rs348555782:231,114,990C/Gintron variant
rs99897352:231,115,454G/T
rs13618051962:231,115,717A/Guncertain significance
rs7550235712:231,115,721G/Auncertain significance
rs24708954892:231,115,771G/Tuncertain significance
rs133851512:231,115,976C/Tintron variant
rs74236152:231,116,874C/Tintron variant
rs7544891612:231,118,103A/Glikely benign
rs286935522:231,119,914G/Cintron variant
rs1383393962:231,120,209G/Cbenign
rs7572584932:231,134,270C/Auncertain significance
rs13960091142:231,134,311C/Auncertain significance
rs7485706622:231,134,617C/Tuncertain significance
rs9197400872:231,134,639C/Tlikely benign
rs1892984362:231,135,293T/Cbenign
rs3773428812:231,135,330T/Auncertain significance
rs24713131712:231,135,352G/Alikely benign
rs2012152212:231,149,074G/Abenign
rs49729462:231,149,108G/Tstop gained
rs3863523642:231,149,112A/Cuncertain significance
rs2020027662:231,150,496T/Guncertain significance
rs7639665982:231,150,512C/Auncertain significance
rs12813190772:231,150,544A/Guncertain significance
rs118871792:231,152,633C/Tbenign
rs2005038072:231,152,634G/Alikely benign
rs3769993502:231,152,639A/Tuncertain significance
rs10091418682:231,152,666A/Guncertain significance
rs2012570532:231,152,673G/Tuncertain significance
rs340044932:231,154,012A/Gintron variant
rs3713186372:231,155,243G/Auncertain significance
rs20572638752:231,157,375T/Cuncertain significance
rs7619677502:231,157,385C/Tuncertain significance
rs3751748982:231,157,435C/Tlikely benign
rs1999597292:231,157,469G/Auncertain significance
rs7608710592:231,157,477G/Tuncertain significance
rs5603743432:231,162,143T/Cuncertain significance
rs621921632:231,175,549T/Cmissense variant
rs7707994762:231,176,168T/Cuncertain significance
rs5339999792:231,176,175G/Cuncertain significance
rs3777052442:231,176,194G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.