B4GALNT3

beta-1,4-N-acetyl-galactosaminyltransferase 3

Summary

B4GALNT3 transfers N-acetylgalactosamine (GalNAc) onto glucosyl residues to form N,N-prime-diacetyllactosediamine (LacdiNAc, or LDN), a unique terminal structure of cell surface N-glycans (Ikehara et al., 2006 [PubMed 16728562]).[supplied by OMIM, Aug 2008]

Known Variants95 total

rsidPosition (GRCh37)AllelesClassClinVar
rs103552251912:569,606C/Auncertain significance
rs14495555212:569,626G/Abenign
rs96867746012:569,645G/Auncertain significance
rs76006177412:569,690G/Auncertain significance
rs254719402612:569,700C/Tuncertain significance
rs796659012:570,840G/C
rs1161247812:574,998G/Aintron variant
rs14133651112:576,618G/Aintron variant
rs713754612:577,237A/C
rs648953912:582,757C/Gintron variant
rs21522312:590,259G/Aregulatory region variant
rs1106320112:590,470G/Aregulatory region variant
rs21522612:591,300A/Gintron variant
rs55763953512:605,652G/A
rs1282112412:608,745C/T
rs1106329612:610,570A/Gintron variant
rs3401952112:618,790G/Cregulatory region variant
rs1183032412:619,618T/G
rs6030957612:623,425G/C
rs15072215412:628,987G/Cintron variant
rs14579825012:644,345G/Cuncertain significance
rs254722614912:644,364C/Guncertain significance
rs14774253412:644,433G/Alikely benign
rs76447383612:653,523C/Guncertain significance
rs74685923712:653,556A/Cuncertain significance
rs57397019312:653,599A/Guncertain significance
rs77066852312:654,076T/Cuncertain significance
rs140065135912:654,111T/Cuncertain significance
rs77805939412:655,816G/Tuncertain significance
rs254723257512:657,198C/Tuncertain significance
rs75881770912:657,251G/Auncertain significance
rs37475576612:657,403C/Tuncertain significance
rs14698673012:657,454C/Tuncertain significance
rs795482512:657,854T/A
rs5889552612:658,104A/T
rs20204034512:658,950A/Glikely benign
rs76008754612:658,965G/Tuncertain significance
rs74533811112:659,031C/Tuncertain significance
rs76891429312:659,049G/Auncertain significance
rs76442102912:659,076G/Auncertain significance
rs19992573412:660,088T/Guncertain significance
rs14488987912:660,114C/Tuncertain significance
rs145232770912:661,253A/Guncertain significance
rs20017345212:661,265C/Tmissense variant
rs37029590512:662,360G/Auncertain significance
rs75530014712:662,405C/Tuncertain significance
rs3541993812:662,412G/Cbenign
rs77182175212:662,446C/Tuncertain significance
rs37283124212:662,515C/Tuncertain significance
rs13810306612:662,516G/Auncertain significance
rs254723649312:662,533C/Tuncertain significance
rs37552088112:662,537G/Alikely benign
rs134521724912:662,566C/Tlikely benign
rs14866513812:662,597C/Tuncertain significance
rs122884639212:662,652G/Tuncertain significance
rs13942162512:662,672A/Tuncertain significance
rs15132164412:662,695C/Tbenign
rs53860270812:662,714C/Guncertain significance
rs15003560212:662,729C/Tuncertain significance
rs76399226012:662,809C/Tlikely benign
rs57820313912:662,824C/Tuncertain significance
rs37156141812:662,825G/Alikely benign
rs76151921412:662,876C/Auncertain significance
rs20221914512:662,878G/Alikely benign
rs37323842612:662,978C/Tuncertain significance
rs15016924812:663,010C/Tuncertain significance
rs36928867212:663,019G/Auncertain significance
rs254723687612:663,071G/Auncertain significance
rs14861308012:663,147G/Cbenign
rs75668627212:665,729C/Tuncertain significance
rs77797549512:665,813C/Tuncertain significance
rs14063339912:665,814G/Auncertain significance
rs77885158812:665,816G/Auncertain significance
rs14515332012:665,822C/Tmissense variant
rs14674919012:665,830G/Alikely benign
rs55386197412:665,888G/Auncertain significance
rs194716028012:665,891G/Cuncertain significance
rs13895540612:665,907G/Tbenign
rs76048236012:665,931G/Auncertain significance
rs254723862512:665,958C/Tuncertain significance
rs14165897312:666,011G/Auncertain significance
rs75979983912:666,839G/Auncertain significance
rs14925084312:666,900T/Clikely benign
rs194718027112:667,241T/Cuncertain significance
rs53932906512:667,249G/Auncertain significance
rs6173039212:667,726G/Clikely benign
rs20109495812:667,744G/Auncertain significance
rs194718834812:667,792G/Tuncertain significance
rs77845346212:668,543G/Cuncertain significance
rs77924956612:670,538G/Auncertain significance
rs20160963312:670,543T/Cuncertain significance
rs36817309112:670,580G/Auncertain significance
rs128070178512:670,585A/Tuncertain significance
rs37174181512:670,597C/Tuncertain significance
rs224089312:672,787G/Aregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.