BAIAP2

BAR/IMD domain containing adaptor protein 2

Summary

The protein encoded by this gene has been identified as a brain-specific angiogenesis inhibitor (BAI1)-binding protein. This adaptor protein links membrane bound G-proteins to cytoplasmic effector proteins. This protein functions as an insulin receptor tyrosine kinase substrate and suggests a role for insulin in the central nervous system. It also associates with a downstream effector of Rho small G proteins, which is associated with the formation of stress fibers and cytokinesis. This protein is involved in lamellipodia and filopodia formation in motile cells and may affect neuronal growth-cone guidance. This protein has also been identified as interacting with the dentatorubral-pallidoluysian atrophy gene, which is associated with an autosomal dominant neurodegenerative disease. Alternative splicing results in multiple transcript variants encoding distinct isoforms.[provided by RefSeq, Jan 2009]

Known Variants64 total

rsidPosition (GRCh37)AllelesClassClinVar
rs250980936317:79,009,101T/Auncertain significance
rs807322417:79,009,153T/Cuncertain significance
rs496923917:79,010,544A/Gregulatory region variant
rs2858551117:79,010,609A/G
rs991347717:79,015,698A/C
rs750293117:79,018,677A/Gregulatory region variant
rs806723517:79,024,637G/Aregulatory region variant
rs807962617:79,026,872A/Gregulatory region variant
rs393449217:79,033,964C/Gintron variant
rs990164817:79,035,708G/T
rs807978117:79,050,148C/Tintron variant
rs496937317:79,050,473A/Gintron variant
rs141748783217:79,058,674A/Guncertain significance
rs37347455017:79,059,504G/Tuncertain significance
rs721043817:79,060,180C/Tintron variant
rs56157127217:79,060,280A/Guncertain significance
rs3589558517:79,060,353T/Abenign
rs496938517:79,068,890C/Tregulatory region variant
rs7263432717:79,072,011A/Guncertain significance
rs931961517:79,072,594A/Cintron variant
rs750221417:79,073,182G/T
rs14493050317:79,073,757C/Tlikely benign
rs14601500617:79,073,793C/Tbenign
rs11140240217:79,073,850G/Abenign
rs14144573817:79,073,862C/Tbenign
rs7595527817:79,077,293C/Tbenign
rs36916763217:79,077,330C/Tuncertain significance
rs77289181817:79,077,378C/Tuncertain significance
rs75886613017:79,077,410G/Auncertain significance
rs14139568617:79,077,413G/Auncertain significance
rs77620904317:79,077,731C/Auncertain significance
rs77265799517:79,077,742C/Tlikely benign
rs14143699817:79,077,746G/Auncertain significance
rs251113636817:79,077,771A/Guncertain significance
rs74695821717:79,077,776C/Tuncertain significance
rs37124984417:79,077,816C/Guncertain significance
rs140661726217:79,077,828C/Tuncertain significance
rs251113851917:79,077,839C/Tuncertain significance
rs156817890517:79,077,881G/Auncertain significance
rs123793931117:79,077,900A/Guncertain significance
rs37773482717:79,078,323A/Guncertain significance
rs3514668817:79,078,423C/Tbenign
rs135758398117:79,078,450C/Glikely benign
rs37679382817:79,079,871C/Tlikely benign
rs55107790317:79,079,942A/Guncertain significance
rs159881369617:79,079,956G/Alikely benign
rs125571969917:79,080,550A/Guncertain significance
rs11573327317:79,080,554A/Gbenign
rs14367862517:79,080,597C/Auncertain significance
rs251123892117:79,080,619A/Guncertain significance
rs92222099717:79,080,634G/Auncertain significance
rs77905477717:79,080,645G/Alikely benign
rs750259017:79,082,081A/Gintron variant
rs1166417:79,082,862G/Auncertain significance
rs407258817:79,084,072G/Tuncertain significance
rs5608416817:79,084,574C/Tregulatory region variant
rs750358017:79,087,036C/Tdownstream gene variant
rs76035991317:79,089,586G/Auncertain significance
rs11710208417:79,089,600G/Abenign
rs75557448817:79,090,071G/Auncertain significance
rs74633959217:79,090,073G/Cuncertain significance
rs77698501117:79,090,085C/Tlikely benign
rs14390517617:79,090,097G/Auncertain significance
rs6207301617:79,090,198C/G

Gene information from NCBI Gene. Variant classifications from ClinVar.