FUT1

fucosyltransferase 1 (H blood group)

Summary

This gene encodes a Golgi stack membrane protein that is involved in the creation of a precursor of the H antigen, which is required for the final step in the synthesis of soluble A and B antigens. This is one of two genes encoding the galactoside 2-L-fucosyltransferase enzyme. Mutations in this gene are a cause of the H-Bombay blood group. [provided by RefSeq, Aug 2016]

Known Variants38 total

rsidPosition (GRCh37)AllelesClassClinVar
rs83814319:49,251,755G/C
rs83814219:49,252,151A/Gupstream gene variant
rs14621690519:49,253,517G/Auncertain significance
rs10489468619:49,253,591G/Cstop gainedaffects
rs251404840419:49,253,600C/Auncertain significance
rs10489468819:49,253,713G/Astop gainedpathogenic
rs83813819:49,253,717G/Tbenign
rs2893458819:49,253,814A/Cmissense variantpathogenic
rs77502022619:49,253,911G/Tuncertain significance
rs76016558319:49,253,913T/Guncertain significance
rs76286049519:49,253,923G/Auncertain significance
rs156849060319:49,253,931C/Tuncertain significance
rs57232796619:49,253,932G/Auncertain significance
rs128499477519:49,253,994C/Tuncertain significance
rs10489468719:49,254,048A/Tmissense variantpathogenic
rs76942865319:49,254,114C/Tlikely benign
rs20156203619:49,254,121G/Auncertain significance
rs76208931719:49,254,128G/Tuncertain significance
rs76528912919:49,254,137T/Guncertain significance
rs78092118219:49,254,167G/Cuncertain significance
rs251404963919:49,254,169A/Guncertain significance
rs76544409119:49,254,173C/Tlikely benign
rs15007405619:49,254,190G/Amissense variantpathogenic
rs77532253019:49,254,205T/Cuncertain significance
rs127801625119:49,254,251A/Glikely benign
rs75315930319:49,254,262T/Cuncertain significance
rs77759853719:49,254,276C/Tuncertain significance
rs75680404319:49,254,286G/Cuncertain significance
rs14468958019:49,254,343C/Guncertain significance
rs251405016119:49,254,372C/Guncertain significance
rs20080826919:49,254,438T/Cuncertain significance
rs14167791819:49,254,482G/Cbenign
rs207169919:49,254,504G/Amissense variantlikely benign
rs15099563219:49,254,519C/Tuncertain significance
rs52961933019:49,255,294C/G
rs169811419:49,259,854A/C
rs169811319:49,259,856T/Cupstream gene variant
rs18396056819:49,260,146G/Aupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.