SGCZ

sarcoglycan zeta

Summary

The zeta-sarcoglycan gene measures over 465 kb and localizes to 8p22. This protein is part of the sarcoglycan complex, a group of 6 proteins. The sarcoglycans are all N-glycosylated transmembrane proteins with a short intra-cellular domain, a single transmembrane region and a large extra-cellular domain containing a carboxyl-terminal cluster with several conserved cysteine residues. The sarcoglycan complex is part of the dystrophin-associated glycoprotein complex (DGC), which bridges the inner cytoskeleton and the extra-cellular matrix. [provided by RefSeq, Jul 2008]

Known Variants53 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7785899338:13,947,995C/Tuncertain significance
rs3716362418:13,948,020G/Auncertain significance
rs1499351028:13,948,082G/Auncertain significance
rs1449790128:13,948,092A/Guncertain significance
rs7581224698:13,948,121T/Clikely benign
rs18016618008:13,948,143A/Guncertain significance
rs11624624478:13,959,906A/Cuncertain significance
rs24861216688:13,959,917T/Cuncertain significance
rs1421368708:13,959,930C/Guncertain significance
rs1905987788:13,965,679C/Auncertain significance
rs1452131898:13,965,705G/Auncertain significance
rs7454280388:13,965,733C/Tuncertain significance
rs126759218:13,989,489G/Aintron variant
rs18041514248:14,022,134C/Auncertain significance
rs70087268:14,067,889A/T
rs3686651958:14,095,104T/Clikely benign
rs132636018:14,095,900A/Cintron variant
rs45670398:14,097,389C/T
rs99427858:14,097,948G/Tintron variant
rs98864288:14,113,816G/Aintron variant
rs132622858:14,125,920C/A
rs78149258:14,154,462C/Gintron variant
rs69900428:14,173,974G/A
rs9295298108:14,181,705C/Tuncertain significance
rs5389605608:14,210,588G/A
rs342690118:14,220,114C/Tintron variant
rs70061788:14,252,384G/Cintron variant
rs74650818:14,262,597A/T
rs732197588:14,279,446G/Aintron variant
rs5410277058:14,298,197C/T
rs24101878:14,356,833G/Aintron variant
rs5773030288:14,362,466T/C
rs19035958:14,389,481A/T
rs8792111498:14,412,261T/Guncertain significance
rs12816910598:14,412,273T/Cuncertain significance
rs2016207858:14,412,299G/Tuncertain significance
rs1494014068:14,412,303C/Tuncertain significance
rs7691900488:14,412,304C/Auncertain significance
rs7531365408:14,412,328T/Guncertain significance
rs12342446118:14,412,344C/Auncertain significance
rs12537625468:14,412,407G/Auncertain significance
rs48316068:14,421,587A/Gintron variant
rs78371648:14,465,681C/Tintron variant
rs736644128:14,486,839G/Cintron variant
rs736644208:14,504,788T/Cintron variant
rs112036498:14,517,294T/Cintron variant
rs119898688:14,550,156A/T
rs48316478:14,630,054A/Gintron variant
rs44271708:14,853,781A/C
rs624953938:14,861,986G/A
rs105035278:14,927,163C/Tintron variant
rs69870118:15,018,745T/Aintron variant
rs5442555768:15,062,306A/C

Gene information from NCBI Gene. Variant classifications from ClinVar.