TBL2

transducin beta like 2

Summary

This gene encodes a member of the beta-transducin protein family. Most proteins of the beta-transducin family are involved in regulatory functions. This protein is possibly involved in some intracellular signaling pathway. This gene is deleted in Williams-Beuren syndrome, a developmental disorder caused by deletion of multiple genes at 7q11.23. [provided by RefSeq, Jul 2008]

Known Variants54 total

rsidPosition (GRCh37)AllelesClassClinVar
rs171457387:72,982,874C/Tdownstream gene variant
rs132321207:72,983,310A/T3 prime UTR variant
rs144157:72,984,780T/A
rs5294936317:72,984,900C/Guncertain significance
rs7819603037:72,984,908G/Auncertain significance
rs7823258057:72,984,913C/Tlikely benign
rs3743014807:72,984,929G/Auncertain significance
rs15545871787:72,984,949T/Cuncertain significance
rs5513171097:72,984,991C/Tuncertain significance
rs7823283357:72,984,997G/Auncertain significance
rs2000127117:72,985,024C/Tuncertain significance
rs1496850737:72,985,072C/Tlikely benign
rs7824873017:72,985,102C/Guncertain significance
rs7827491447:72,985,165A/Guncertain significance
rs7820713457:72,985,174C/Tuncertain significance
rs7827025637:72,985,179C/Tlikely benign
rs1464375327:72,985,185G/Alikely benign
rs3712434967:72,985,238T/Glikely benign
rs15545873577:72,985,253C/Tuncertain significance
rs2009523417:72,985,281A/Tuncertain significance
rs1998289217:72,985,305G/Alikely benign
rs1850800247:72,985,522C/Tconflicting classifications of pathogenicity
rs7820015877:72,985,559C/Tuncertain significance
rs15840241197:72,985,590C/Alikely benign
rs17929353837:72,985,625C/Tuncertain significance
rs1417393957:72,985,627T/Gbenign
rs1456015057:72,985,664C/Auncertain significance
rs17930496867:72,987,198T/Guncertain significance
rs5430148027:72,987,209C/Tuncertain significance
rs617367417:72,987,212C/Tbenign
rs1486026527:72,987,226T/Cuncertain significance
rs7823068557:72,987,270G/Cuncertain significance
rs7827810297:72,987,292T/Cuncertain significance
rs22862767:72,987,354C/Tregulatory region variant
rs1412090317:72,987,681C/Tlikely benign
rs356591267:72,988,069C/Tintron variant
rs7823396497:72,988,298G/Auncertain significance
rs7823205087:72,988,305C/Tuncertain significance
rs785296617:72,988,309C/Tbenign
rs5531219957:72,988,316T/Cuncertain significance
rs2005349767:72,988,326T/Guncertain significance
rs1410027367:72,988,371G/Auncertain significance
rs1873595227:72,988,709G/Alikely benign
rs2020927257:72,988,777C/Tuncertain significance
rs5576387487:72,988,784A/Glikely benign
rs5401337537:72,988,807G/Alikely benign
rs15840335287:72,989,141C/A
rs353486637:72,991,593G/A
rs125400117:72,991,704G/Aregulatory region variant
rs2013370537:72,992,763G/Tlikely benign
rs24851615547:72,992,764C/Tuncertain significance
rs15545895197:72,992,795G/Auncertain significance
rs7818662307:72,992,860G/Auncertain significance
rs126668837:72,994,476C/T

Gene information from NCBI Gene. Variant classifications from ClinVar.