CYP2A6

cytochrome P450 family 2 subfamily A member 6

Pharmacogene

Summary

This gene, CYP2A6, encodes a member of the cytochrome P450 superfamily of enzymes. The cytochrome P450 proteins are monooxygenases which catalyze many reactions involved in drug metabolism and synthesis of cholesterol, steroids and other lipids. This protein localizes to the endoplasmic reticulum and its expression is induced by phenobarbital. The enzyme is known to hydroxylate coumarin, and also metabolizes nicotine, aflatoxin B1, nitrosamines, and some pharmaceuticals. Individuals with certain allelic variants are said to have a poor metabolizer phenotype, meaning they do not efficiently metabolize coumarin or nicotine. This gene is part of a large cluster of cytochrome P450 genes from the CYP2A, CYP2B and CYP2F subfamilies on chromosome 19q. The gene was formerly referred to as CYP2A3; however, it has been renamed CYP2A6. [provided by RefSeq, Jul 2008]

Known Variants68 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14373139019:40,843,969T/Amissense variant
rs819273019:40,844,677C/Gmissense variant
rs2839946319:40,844,682T/Cmissense variantbenign
rs37681765719:40,844,766C/Tmissense variant
rs14816681519:40,845,404A/Gmissense variant
rs76346958419:40,846,903A/Gmissense variant
rs14047170319:40,846,912C/Tmissense variant
rs2839944519:40,848,263TGC/TAframeshift variant
rs56881180919:40,848,284CTT/Cframeshift variant
rs19991611719:40,848,293T/Cmissense variant
rs6056353919:40,848,629G/Tmissense variant
rs6060588519:40,848,633G/Cmissense variant
rs5955235019:40,848,716A/Cmissense variant
rs498689119:40,848,724C/Amissense variant
rs283994019:40,848,755A/Gmissense variant
rs7254943519:40,849,833C/Gmissense variant
rs19954520019:40,849,860G/Astop gained
rs14369036419:40,849,959C/Tmissense variant
rs7254943219:40,850,411T/Gmissense variantbenign
rs2839943419:40,850,414C/Tmissense variant
rs55674395119:41,349,197A/G
rs225921719:41,349,233A/Gdownstream gene variant
rs2839948319:41,349,497G/T
rs2839946819:41,349,732C/Amissense variant
rs5853720119:41,349,746A/Gbenign
rs503101719:41,349,750C/Amissense variant
rs251603446819:41,349,766A/Guncertain significance
rs503101619:41,349,774A/Gmissense variant
rs76142291819:41,349,802G/Alikely benign
rs14333616519:41,350,600G/Abenign
rs5631411819:41,350,630A/Glikely benign
rs15058623419:41,351,211G/Asynonymous variant
rs78114008619:41,351,214A/Cuncertain significance
rs2839945419:41,351,267C/Tmissense variant
rs75742841919:41,351,288C/Tuncertain significance
rs37420010919:41,351,354C/Tuncertain significance
rs251603704619:41,351,381C/Tlikely benign
rs14443738419:41,351,563G/C
rs14869308419:41,351,935A/Guncertain significance
rs499755719:41,351,953G/Cmissense variant
rs76606474819:41,351,956A/Guncertain significance
rs74609579219:41,351,997C/Tlikely benign
rs118294321819:41,352,784T/Guncertain significance
rs78012912819:41,352,791G/Auncertain significance
rs77608781519:41,352,818G/Cuncertain significance
rs37478408319:41,352,858C/Auncertain significance
rs14514872119:41,352,884C/Tuncertain significance
rs2839944819:41,352,936C/Tsynonymous variant
rs2839944719:41,352,941A/Gmissense variantdrug response
rs5611385019:41,353,107T/Cintron variant
rs5626734619:41,353,338A/Gintron variant
rs5592159319:41,353,897G/Tintron variant
rs18554556019:41,354,143G/Auncertain significance
rs5625650019:41,354,171G/Tmissense variant
rs57133558719:41,354,209C/Alikely benign
rs144438808519:41,354,239T/Cuncertain significance
rs180127219:41,354,533A/Tmissense variantdrug response
rs77277265019:41,354,540C/Auncertain significance
rs251604190919:41,354,548A/Cuncertain significance
rs196714690419:41,354,644C/Tuncertain significance
rs7254943419:41,355,754T/Clikely benign
rs57726765019:41,355,786G/Tuncertain significance
rs36835950719:41,355,802C/Auncertain significance
rs19951534219:41,355,876G/Alikely benign
rs14970328119:41,356,313G/Auncertain significance
rs2839943319:41,356,379A/G
rs6721056719:41,357,457G/Tupstream gene variant
rs726062919:41,357,632T/A

Gene information from NCBI Gene. Variant classifications from ClinVar.