PCCB

propionyl-CoA carboxylase subunit beta

Summary

The protein encoded by this gene is a subunit of the propionyl-CoA carboxylase (PCC) enzyme, which is involved in the catabolism of propionyl-CoA. PCC is a mitochondrial enzyme that probably acts as a dodecamer of six alpha subunits and six beta subunits. This gene encodes the beta subunit of PCC. Defects in this gene are a cause of propionic acidemia type II (PA-2). Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, May 2010]

Known Variants836 total

rsidPosition (GRCh37)AllelesClassClinVar
rs37556363:135,968,828C/Gbenign
rs1146663633:135,969,063C/Tlikely benign
rs168438063:135,969,078C/Glikely benign
rs7518371623:135,969,172A/Tuncertain significance
rs1457341573:135,969,181C/Tlikely benign
rs8860580163:135,969,183G/Auncertain significance
rs3726497753:135,969,184G/Auncertain significance
rs15537731413:135,969,206G/Alikely benign
rs3981234623:135,969,219T/Amissense variantpathogenic
rs3981234643:135,969,220G/Amissense variantpathogenic
rs7480033963:135,969,222C/Auncertain significance
rs7698353563:135,969,223G/Alikely benign
rs3736853723:135,969,225C/Tuncertain significance
rs7630251143:135,969,226G/Clikely benign
rs14768764453:135,969,229A/Glikely benign
rs15599919213:135,969,230T/Clikely benign
rs12924524853:135,969,231T/Gpathogenic
rs3776817683:135,969,233C/Tuncertain significance
rs7679658143:135,969,234G/Tuncertain significance
rs21081277023:135,969,235G/Clikely benign
rs13060529883:135,969,236G/Tuncertain significance
rs14047630213:135,969,238G/Alikely benign
rs7646020193:135,969,240C/Tuncertain significance
rs10575236113:135,969,241G/Tlikely benign
rs14024044073:135,969,244G/Alikely benign
rs7543033183:135,969,247C/Alikely benign
rs7578601523:135,969,248G/Cuncertain significance
rs12305635873:135,969,251G/Auncertain significance
rs12574392753:135,969,252C/Auncertain significance
rs19414770303:135,969,255G/Auncertain significance
rs7511895673:135,969,256G/Alikely benign
rs12157059983:135,969,257C/Tuncertain significance
rs21081277833:135,969,259C/Tlikely benign
rs7546645633:135,969,262C/Tconflicting classifications of pathogenicity
rs7808420043:135,969,263G/Tuncertain significance
rs15763975313:135,969,265T/Clikely benign
rs2001857473:135,969,266C/Aconflicting classifications of pathogenicity
rs12624649043:135,969,268G/Alikely benign
rs7694814503:135,969,270C/Guncertain significance
rs13436186923:135,969,271G/Alikely benign
rs11969953783:135,969,274C/Tlikely benign
rs7777267173:135,969,275G/Auncertain significance
rs19414786183:135,969,280C/Glikely benign
rs7711172633:135,969,281C/Tuncertain significance
rs7598369963:135,969,283C/Glikely benign
rs7724832503:135,969,284G/Auncertain significance
rs25297314693:135,969,285C/Tuncertain significance
rs5593205643:135,969,286C/Tlikely benign
rs13893537043:135,969,289G/Tlikely benign
rs9689299733:135,969,290G/Auncertain significance
rs7610304223:135,969,292C/Tlikely benign
rs25297315503:135,969,295C/Alikely benign
rs1411376913:135,969,299C/Guncertain significance
rs7658434103:135,969,303G/Tuncertain significance
rs25297316233:135,969,305A/Guncertain significance
rs7511361393:135,969,311G/Auncertain significance
rs21081279073:135,969,312C/Tuncertain significance
rs21081279123:135,969,313C/Tlikely benign
rs19414805013:135,969,316C/Glikely benign
rs12172045173:135,969,319T/Clikely benign
rs19414807593:135,969,323A/Cuncertain significance
rs12082056723:135,969,332A/Guncertain significance
rs1824122703:135,969,333T/Cuncertain significance
rs7558892663:135,969,336A/Guncertain significance
rs10319419893:135,969,344C/Tuncertain significance
rs19414818633:135,969,345G/Auncertain significance
rs19414819393:135,969,346C/Tlikely benign
rs7492103743:135,969,347C/Tuncertain significance
rs3750142733:135,969,348G/Auncertain significance
rs9591636943:135,969,349G/Tlikely benign
rs12947108983:135,969,351C/Guncertain significance
rs15763976283:135,969,352C/Alikely benign
rs1450758173:135,969,355G/Clikely benign
rs1999353803:135,969,356C/Guncertain significance
rs9160832003:135,969,357T/Guncertain significance
rs13788079523:135,969,358G/Alikely benign
rs3769837093:135,969,359C/Tlikely benign
rs13685864453:135,969,360T/Guncertain significance
rs14624119283:135,969,361G/Clikely benign
rs21081280433:135,969,367G/Clikely benign
rs7472142503:135,969,368G/Auncertain significance
rs11982149903:135,969,375G/Auncertain significance
rs7769007643:135,969,376C/Tlikely benign
rs13285955943:135,969,378G/Auncertain significance
rs5615395463:135,969,380A/Guncertain significance
rs7657902113:135,969,381T/Cuncertain significance
rs7737144433:135,969,382T/Clikely benign
rs19414845363:135,969,383G/Tuncertain significance
rs14225278523:135,969,384A/Guncertain significance
rs7590084773:135,969,385C/Tlikely benign
rs3714060483:135,969,386G/Auncertain significance
rs2006369683:135,969,387C/Tuncertain significance
rs11680772733:135,969,388G/Tlikely benign
rs7639492763:135,969,390A/Clikely pathogenic
rs15763977013:135,969,391G/Alikely benign
rs1479543633:135,969,392C/Alikely pathogenic
rs7571348773:135,969,394C/Gconflicting classifications of pathogenicity
rs1406368703:135,969,397G/Aconflicting classifications of pathogenicity
rs9095500053:135,969,399G/Auncertain significance
rs3981234603:135,969,401G/Apathogenic

Showing 100 of 836 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.