ZNRF3

zinc and ring finger 3

Summary

Enables frizzled binding activity and ubiquitin-protein transferase activity. Involved in negative regulation of Wnt signaling pathway; protein ubiquitination; and ubiquitin-dependent protein catabolic process. Located in plasma membrane. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants82 total

rsidPosition (GRCh37)AllelesClassClinVar
rs102535068122:29,279,823C/Glikely benign
rs251827295122:29,279,901G/Tlikely benign
rs251827299122:29,279,920A/Guncertain significance
rs14035381922:29,296,224G/Aintron variant
rs1698682522:29,300,306C/Tregulatory region variant
rs7514164022:29,319,152T/Cintron variant
rs728602622:29,333,861C/Gintron variant
rs2836061522:29,338,656G/Cintron variant
rs576290722:29,339,085C/G
rs575284022:29,348,003C/Tregulatory region variant
rs251753291922:29,383,074T/Cpathogenic
rs7768861022:29,415,725A/Gdownstream gene variant
rs14559815622:29,416,402C/Tdownstream gene variant
rs251758592322:29,439,321C/Tpathogenic
rs37184116722:29,440,768C/Auncertain significance
rs75747729222:29,440,813G/Auncertain significance
rs77252039322:29,440,868G/Auncertain significance
rs127276881722:29,442,744T/Cuncertain significance
rs75918431422:29,442,783G/Auncertain significance
rs77495816922:29,442,789G/Auncertain significance
rs251758974522:29,442,837G/Aconflicting classifications of pathogenicity
rs251758975322:29,442,846G/Apathogenic
rs251759140522:29,444,384G/Apathogenic
rs251759147022:29,444,420G/Apathogenic
rs75846669222:29,444,428C/Tuncertain significance
rs251759149622:29,444,429C/Gpathogenic
rs37279062922:29,444,458C/Guncertain significance
rs37572311122:29,444,459A/Guncertain significance
rs251759156722:29,444,464C/Tpathogenic
rs75977732122:29,445,277G/Auncertain significance
rs251759267622:29,445,316A/Guncertain significance
rs146718004022:29,445,457G/Auncertain significance
rs3467130322:29,445,468C/Tbenign
rs96633400022:29,445,482G/Auncertain significance
rs74587004922:29,445,580C/Tuncertain significance
rs203714419622:29,445,589T/Cuncertain significance
rs19300413022:29,445,615G/Cuncertain significance
rs77455262722:29,445,619G/Auncertain significance
rs18422832522:29,445,676G/Auncertain significance
rs36829426322:29,445,712G/Alikely benign
rs89532832722:29,445,739G/Auncertain significance
rs115795636722:29,445,767A/Guncertain significance
rs20073535922:29,445,841G/Auncertain significance
rs20161114622:29,445,852C/Auncertain significance
rs75883395022:29,445,950A/Guncertain significance
rs251759421022:29,445,967C/Tuncertain significance
rs147525996822:29,446,013G/Cuncertain significance
rs77062200522:29,446,051C/Tuncertain significance
rs19989237522:29,446,070C/Tuncertain significance
rs36789454222:29,446,073C/Tlikely benign
rs37510669622:29,446,249G/Tuncertain significance
rs116490705622:29,446,280G/Tuncertain significance
rs141583672722:29,446,328C/Auncertain significance
rs20148333322:29,446,367T/Cuncertain significance
rs18959013722:29,446,401C/Tbenign
rs147684985722:29,446,417C/Tuncertain significance
rs76774018522:29,446,480G/Auncertain significance
rs91657617322:29,446,513T/Cuncertain significance
rs74684042522:29,446,544G/Auncertain significance
rs212388906822:29,446,577C/Guncertain significance
rs77917481522:29,446,584T/Auncertain significance
rs123651790622:29,446,595C/Tuncertain significance
rs137595623022:29,446,637G/Auncertain significance
rs100594949822:29,446,658C/Guncertain significance
rs251759584322:29,446,670A/Tuncertain significance
rs77111676022:29,446,709A/Guncertain significance
rs77940595522:29,446,771A/Guncertain significance
rs19955037922:29,446,787C/Guncertain significance
rs76994140322:29,446,802G/Alikely benign
rs76422155022:29,446,835G/Auncertain significance
rs36829857322:29,446,861G/Auncertain significance
rs140464522822:29,446,867G/Auncertain significance
rs251759621822:29,446,870A/Tuncertain significance
rs77237538422:29,449,570C/Tuncertain significance
rs53689188222:29,449,600C/Tuncertain significance
rs6223688122:29,450,193G/Aregulatory region variant
rs729011722:29,450,856C/G
rs217912922:29,450,923A/Gdownstream gene variant
rs482300622:29,451,671A/Gregulatory region variant
rs320880022:29,451,793G/T
rs482300722:29,452,278A/T
rs317891522:29,453,027A/Gdownstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.